C C45327 Hydroa Vacciniforme-Like Lymphoproliferative Disorder Hydroa Vacciniforme-Like Lymphoma HV-Like Lymphoma A rare, EBV-positive cutaneous T-cell lymphoproliferative disorder, composed of CD8 positive cytotoxic T-lymphocytes. It affects children, almost exclusively in Latin America and Asia. Patients present with papulovesicular skin lesions, clinically resembling hydroa vacciniforme, in areas of sun-exposed skin. In contrast to hydroa vacciniforme (HV), HV-like lymphoma is not induced by sun exposure and the lesions can occur in both sun-exposed and covered body areas. It affects children, almost exclusively in Latin America and Asia. C3211 Non-Hodgkin Lymphoma C90259 Pediatric Terminology C C80297 Pediatric-Type Follicular Lymphoma Childhood Follicular Lymphoma Pediatric Follicular Lymphoma A nodal follicular lymphoma with favorable prognosis. It lacks BCL-2 rearrangement and 14;18 translocation. Nearly all cases are localized. It is usually seen in the pediatric population but similar lymphomas may occur in adults. A variant of follicular lymphoma seen in children and adolescents that lacks the translocation of t(14;18)(q32;q21) involving BCL2, which is generally found in adults. C7706 Childhood Non-Hodgkin Lymphoma C90259 Pediatric Terminology C C80374 Systemic EBV-Positive T-Cell Lymphoma of Childhood Systemic EBV-Positive T-Cell Lymphoproliferative Disease of Childhood An aggressive and life-threatening, EBV-positive T-cell lymphoma affecting children. It is more prevalent in Taiwan and Japan. Clinically, it presents with acute onset of fever and generalized malaise, followed by hepatosplenomegaly and liver failure. Morphologically it is characterized by the presence of infiltrating T-lymphocytes which are usually small and erythrophagocytosis. Most patients have a fulminant clinical course. An aggressive, life-threatening, EBV-positive T-cell lymphoproliferative disorder affecting children. C26323 Hematologic Disorder C90259 Pediatric Terminology C C5637 Childhood Mature T-Cell and NK-Cell Non-Hodgkin Lymphoma Childhood Mature T- and NK-Cell Lymphoma A mature T- and NK-cell non-Hodgkin lymphoma that occurs during childhood. A mature T- and NK-cell non-Hodgkin lymphoma that occurs during childhood. C7706 Childhood Non-Hodgkin Lymphoma C90259 Pediatric Terminology