C	C3444	Granulomatosis with Polyangiitis	Granulomatosis with Polyangiitis	GPA|Wegener Granulomatosis|Wegener's Granulomatosis	A rare, autoimmune, systemic medium and small size vasculitis. It is characterized by the formation of necrotizing granulomas in the respiratory tract, necrotizing angiitis, and glomerulonephritis.	Systemic vasculitis affecting small to medium-sized vessels, characterized by necrotizing granulomas in the respiratory tract, necrotizing angiitis, glomerulonephritis with little to no immune complex deposition, and typically positive for antineutrophil cytoplasmic antibody staining in a cytoplasmic pattern (C-ANCA; antiproteinase 3).	C26912	Vasculitis			C118468	Pediatric Rheumatology Terminology